SUSPECTED CHIASMATIC PATHOLOGY IN PAZIENT AFFECTED BY ATYPICAL SECTOR RETINITIS PIGMENTOSA: THE IMPORTANCE OF CLINICAL AND STRUMENTAL VALUES

摘要

Retinitis pigmentosa (RP) is one of the most common hereditary retinal dystrophies and causes of visual impairment affecting all age groups. Sector retinitis pigmentosa is an atypical form of RP that is characterized by regionalized areas of bone spicule pigmentation, usually in the inferior quadrants of the retina. Tipically it presents symmetric and bilateral. Sector RP has a variable symptomatology: night vision decrease (nictalopia), photophobia, visual field constrinction, with partial or complete scotoma. However, any pazients may remain asimpthomatic until adulthood.