Constriction band syndrome is set of congenital birth defects caused by entrapment of fetal parts usually a limb or digits in fibrous amniotic bands while in the uterus. It is also known as amniotic band sequence, streeter dysplasia, congenital bands or rings and amniotic adhesions mutilations Case presentation Our patient is a 6 days old male baby, first in birth order and product of a non consanguineous marriage .The patient was born with congenitally abnormal right hand. On thorough examination, the patient has bilateral talipes equinovarus in addition to abnormal right hand. In the right hand, the thumb is normal, the index finger has amputated distal phalanx, the middle and the ring finger each has amputated distal phalanx and each bears a constriction ring at the level of middle phalanx and the little finger has amputated middle and distal phalanx. The patient has been attached to outpatients department for follow-up of hand defect .The worried parents were counseled and reassured that the disease has no proven familial link and that the abnormality in their first child does not increase the possibility of constriction/auto amputations in future offspring.
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