Rare Presentation of Superficial Leiomyosarcoma of Scalp

摘要

Leiomyosarcomas are uncommon malignant smooth muscle tumours, mainly derived from vessels or viscera. Superficial leiomyosarcomas are rare, represent only 7 - 10 % of leiomyosarcoma cases. Superficial leiomyosarcomas can be primary or secondary. Primary superficial leiomyosarcomas arise from the dermis (cutaneous leiomyosarcoma) or subcutaneous tissue (subcutaneous leiomyosarcoma) in the skin. They have distinctly different histologic and prognostic features from each other. The most affected parts being the extremities, especially lower extremities, followed by head and neck region. In head and neck region, primary tumors are present in only 3 - 10% of cases. We present the case of a 48 year old female, with no family history of malignancy, diagnosed with primary superficial leiomyosarcoma of scalp with frontal bone lysis and intracranial extension. The peculiarity of this case is the rarity of this tumor, uncommon location and bone involvement which has been seen only in approximately 10% of the cases.