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Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review

机译:位置总反转的特发性血小板减少性紫癜:病例报告和文献复习

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摘要

is a rare recessive autosomal congenital abnormality in which the mediastinal and abdominal organs are in a mirrored position when compared to the usual topography. The literature reports some cases of and concomitant conditions: spinal abnormalities, cardiac malformations and hematological diseases, such as idiopathic thrombocytopenic purpura, which is an autoimmune disease that causes thrombocytopenia due to platelet destruction or suppression of its production. This article aimed to report the coexistence of and idiopathic thrombocytopenic purpura.
机译:是一种罕见的隐性常染色体先天性异常,与常规地形相比,纵隔和腹部器官处于镜像位置。文献报道了一些并发疾病的情况:脊柱异常,心脏畸形和血液病,例如特发性血小板减少性紫癜,这是一种自身免疫性疾病,由于血小板破坏或抑制血小板生成而导致血小板减少。本文旨在报告与特发性血小板减少性紫癜并存。

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