Hypoxia due to intrapulmonary vascular dilatation in a toddler with a congenital portacaval shunt: case report

摘要

BackgroundThe term hepatopulmonary syndrome typically applies to cyanosis that results from “intrapulmonary vascular dilatation” due to advanced liver disease. Similar findings may result from a congenital portosystemic shunt without liver disease. An adverse consequence of such shunts is intrapulmonary vascular dilatation, which affects the microvascular gas exchange units for oxygen.