In this article, an interesting case of Apert syndrome in a 14-year-old boy with characteristic craniosynostosis, acrocephaly, midface hypoplasia, pharyngeal attenuation, ocular manifestations, and syndactyly of the hands and feet is presented. The case is discussed in the light of relevant literature. A precise clinical differentiation must be made since considerable overlap of the features of various other syndromes could give rise to difficulties in diagnosing this condition. Besides detection and timely recognition of the syndrome to allow adequate dental care, screening at periodic intervals is merited to improve the overall quality of life of these patients. >Clinical relevance class="enumerated" style="list-style-type:decimal">This paper highlights the importance of the dentist aswell as the specialist in the recognition and oral care ofchildren with this syndrome.Children with teeth of unusual anatomy present achallenge for conventional dentistry.It is important for a pedodontist to evaluate and intervenethe malrelationship of the jaws to reduce the complexityof further orthodontic treatment.>Objectives statement: The reader should understand theclinical implications of recognition of this syndrome andprovision of early treatment, with a purpose to reducing theduration and complexity of further treatment.
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