Objective To study the diagnosis and differential diagnosis of type Ⅰ Madelung's disease by CT imaging. Methods The CT imaging and clinical data of 6 patients with typeⅠ Madelung's disease were retrospectively analyzed. Results CT imaging showed no capsule adipose tissue density that was distributed widely and diffusely,most patients with adipose tissue deposition in the occipital,neck,shoulder,supraclavicular and sternal area,etc;of which 2 cases,trachea and muscle were compressed by adipose tissue that displacement and morphological changes;5 patients had alcohol history,1 patient had no history of alcoholism. The average age was 54.5±13.4 years old;2 cases of low weight that BMI less than<18.5kg/m2;3 cases of abnormal liver function;thyroid function decreased in 1 case;nocturnal sleep snoring in 3 cases;2 cases of surgery with a good recovery and no recurrence. Conclusion CT can clearly show the widely distributed adipose density tissue of type Ⅰ Madelung's disease, it also shows that the relationship with the surrounding tissue. Combined with the clinical data,it is significance value in the diagnosis and differential diagnosis of type Ⅰ Madelung's disease.%目的 探讨Ⅰ型马德龙病的CT影像诊断及鉴别诊断.方法 回顾分析6例Ⅰ型马德龙病患者的CT影像学资料及临床资料.结果 CT影像表现为较广泛、弥漫分布的均一对称的无包膜脂肪组织低密度影,大多数患者脂肪组织沉积部位在枕部、颈项部、肩背部、锁骨上及胸骨上区域等,其中2例气管及肌肉等被脂肪组织压迫移位及形态改变;临床上5例患者具有酗酒史,1例否认酗酒史;平均年龄(54.5±13.4)岁;2例BMI<18.5kg/m2,为低体重;肝功能异常3例;甲状腺功能减低1例;夜间睡眠打鼾3例;手术2例,恢复良好,无复发.结论 CT可清晰显示Ⅰ型马德龙病广泛分布的脂肪密度组织及其与周围组织关系,结合临床资料,CT在Ⅰ型马德龙病的诊断及鉴别上具有重要价值.
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