IgG4相关性疾病是近年来新认识的一种疾病,是由免疫介导的累及身体多个器官或组织的慢性自身免疫系统疾病。本文就IgG4相关性慢性硬化性颌下腺炎的临床表现、组织病理学、影像学表现、治疗方式等最新进展做一综述。%In recent years,IgG4-related disease has been knowed as a new disease. It is a chronic immune-mediated autoimmune diseases involving multiple body organs or tissues. This article,we will review thelatest developments of IgG4 - related Chronic Sclerosing Sialadenitis, through itchiest pathology,imaging,treatment and so on.
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