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Management and evaluation of bladder paragangliomas

         

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Dear editor,Extraadrenal paragangliomas are tumors composed of neuroendocrine-derived,catecholamine-secreting chromaffin cells inducing hypertension,palpitations,and diaphoresis[1].Although extraadrenal paragangliomas are found in a variety of anatomic sites that normally host paraganglia—from the carotid body to the abdominal paraaortic region—the bladder is an uncommon location for paragangliomas.Bladder paragangliomas represent approximately 6%of extraadrenal paragangliomas and only 0.05%of all bladder tumors[2,3].We present a rare case of primary paraganglioma affecting the bladder dome.

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