Oesophageal atresia and tracheoesophageal fistula with right pulmonary agenesis and duplication of the azygos vein

摘要

A premature (35 weeks' gestation) girl developed respiratory-distress immediately after birth along with frothing from the mouth. A nasogastric tube could not be passed. Breath sounds were absent on the right side of the chest and the cardiac apex beat was located on the right side. Chest x-ray revealed opacification of the right hemithorax, absence of the right lung shadow, apparent dextrocardia and a hyperaerated left lung crossing the midline (figure 1). The upper oesophagus with the feeding tube coiled in it was deviated to the right. Thoracotomy revealed absence of the right lung, two azy-gos veins adjacent to each other, each with three tributaries (figure 2), and a right-sided aortic arch. The patient had oesoph-ageal atresia (OA) with distal tracheoesophageal fistula (TEF) which was repaired. The baby died on the third postoperative day from progressive respiratory failure.