Technique of Lung Isolation for Whole Lung Lavage in a Child with Pulmonary Alveolar Proteinosis

摘要

PULMONARY alveolar proteinosis is a rare disease in which accumulation of phospholipoproteinaceous material in the alveoli causes pulmonary impairment.1 A deficiency in granulocyte-macrophage colony-stimulating factor activity results in defective macrophages and reduced clearance of surfactant from the lungs.1'2 Bronchoalveolar or whole lung lavage is an important part of treatment for this disease and often results in temporary improvement of symptoms and radiographic appearance