Imaging and histopathologic findings of desmoplastic small round cell tumor

摘要

To the Editor, Abdominal desmoplastic small round cell tumor (DSRCT) is an extremely rare malignancy (1). It typically affects young men with an aggressive clinical course (2). A 23-year-old male presented with constipation and poorly localized dull abdominal pain lasting for one month. He also suffered from poor appetite and unintentional weight loss. Abdominal examination revealed a palpable lower abdominal mass. Blood chemistry and tumor markers were unremarkable except for increased CA-125 (130 U/mL). Abdominopelvic ultrasound (US) demonstrated a macrolobulated heterogeneous pelvic mass measuring 12x10 cm with a mixed solid and cystic pattern extending to epigastrium with an unclear origin (Fig. 1 A). Contrast-enhanced computed tomography (CT) depicted multiple large and lobulated masses (Fig 1B to D).