Congenital absence of the inferior vena cava: a rare risk factor for idiopathic deep-vein thrombosis.

摘要

A 39-year-old man in good health presented to our hospital with acute swelling of the left leg. No risk factors for deep venous thrombosis (DVT) were present, in particular, no immobilization, surgery, known thrombophilia, or family history. Venous duplex ultrasonography demonstrated complete thrombosis of the left iliac and femoral veins, and the inferior vena cava was not detectable. Abdominal magnetic resonance angiography (Cover) confirmed the absence of the infrarenal portion of die vena cava. The renal veins (R) drained into dilated lumbar veins (L), and only at the intrahepatic level was the diameter of the vena cava inferior normal (A). The hemiazygos vein (H) was dilated as a compensatory mechanism, and as anatomically expected, the thoracic dilated hemiazygos system drained into the dilated azygos vein (Az) (B). No congenital defects of the heart or abdominal organs were seen.