Epimyocardium-dominant electrical impairment in a patient with cardiolaminopathy.

摘要

A 41-year-old male was referred to us to undergo catheter ablation against an electrical storm of sustained ventricular tachycardia (VT) (Fig. 1A) accompanied with dilated car-diomyopathy (DCM). Echocardiography demonstrated a left ventricular ejection fraction of 39%. His mother died because of cardiac disease in her 30s, but the details remain unknown. He had a previous history of the implantation of a pacemaker for advanced atrioventricular conduction block (AVB) accompanied by atrial fibrillation (AF) at the age of 32, a failed catheter ablation against sustained VT by an endocardial approach followed by the implantation of an im-plantable cardioverter defibrillator at the age of 39, and the upgrade to a cardiac resynchronization therapy defibrillator device at the age of 40.