Cardiac fbromas are rare tumours of the heart. We present a case of cardiac fbroma in a four-year-old child in view of rarity of the caseand success achieved in its management. The child had presented with a history of intermittent palpitations. Electrocardiography(ECG) showed monomorphic Ventricular Tachycardia (VT). She was initially managed with intravenous Metoprolol and Amiodaroneinfusion but had recurrent VT. Echocardiography revealed a mass in the apical septum. A Contrast Enhanced Computed Tomography(CECT) showed a homogeneous mass involving the anterolateral and apical aspect of interventicular septum causing expansion ofthe septum and indentation and compression of both ventricles. The tumour was approached through median sternotomy underCardiopulmonary Bypass (CPB). The adventitia over the exposed part of the tumour was incised and the tumour was dissected outof the interventricular septum. A bovine pericardial patch was used to close the septal defect. Most of the small tumours dispersedaround Left Anterior Descending Artery (LAD) were excised. The patient was weaned off CPB easily.In the postoperative period, Amiodarone infusion was continued with no recurrence of arrhythmias. Histopathology revealedclassical features of fbroma. The child is stable and is on outpatient follow-up.Our patient had a huge fbroma and we could successfully resect it avoiding need for transplant. We hereby conclude that inchildren with a huge intracardiac fbroma involving almost a complete cardiac chamber, success can be achieved through resectionand reconstruction in selected cases and the need for transplant may be obviated.
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