Portal biliopathy (PB) is defined as biliary obstruction associated with enlarged collaterals in the setting of chronic extrahepatic portal vein occlusion (portal vein thrombosis EHPVO) or cavernous transformation of the portal vein. Although patients with portal biliopathy normally have asymptomatic biliary dilatation or an increase in liver enzyme levels, they may rarely experience jaundice, cholangitis, or choledocholithiasis. The present case is of a 17-year-old male presenting with obstructive jaundice, malena, cholelithiasis secondary to portal venous thrombosis and cavernous transformation of portal vein due to CBD stricture secondary to portal hypertensive biliopathy (PHB).
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