Clinical Dilemma: Recurrent Syncope With Isolated Left Ventricle Non-Compaction Cardiomyopathy and Preserved Ejection Fraction, a Case Report and Review of the Literature

摘要

Left ventricle non-compaction cardiomyopathy (LVNC) is an uncommon disorder characterized by the persistence of fetal myocardium of prominent trabecular meshwork, deep intertrabecular recesses, systolic dysfunction and left ventricular dilatation. It is thought to be caused by the arrest of normal endomyocardial morphogenesis. Here we present a case of a 27-year-old Caucasian female without past medical history who was presented to the emergency department because of syncope while she was working out. On further questioning, she relates that she has been having recurrent syncope for the last 9 years but she did not seek medical attention. Echocardiography and cardiac magnetic resonance imaging confirmed the diagnosis of LVNC and also showed a preserved ejection fraction. Implantable loop recorder showed recurrent non-sustained ventricular tachycardia. Although data were limited, an implantable cardioverter-defibrillator was prophylactically implanted because of the individual’s high sudden cardiac death risk.J Med Cases. 2015;6(2):77-80doi: http://dx.doi.org/10.14740/jmc2035w