The new ATS-ERS-JRS-ALAT Guidelines for diagnosis of Idiopathic Pulmonary Fibrosis (IPF)

摘要

Idiopathic Pulmonary Fibrosis (IPF) is the most frequent idiopathic interstitial“pneumonia”1-3 and one of the almost 500 interstitial lung diseases.IPF is a specific form of chronic, progressive fibrosing interstitial pneumoniaof unknown cause occurring in adults. Radiologic and/or histopathologicpatterns are consistent with usual interstitial pneumonia (UIP)4-6.