Isolated intra-axial central nervous system juvenile xanthogranuloma (JXG). Clinical management and follow-up with PET-MRI

摘要

Juvenile xanthogranuloma (JXG) is the most common non-Langerhans histiocytic disorder, it is benign and self-limited [1]. It is a typical disorder in early childhood (80–90% of patients are children under 2 years old) and most cases present as a solitary reddish or yellowish skin papule or nodule on the head, neck, or upper trunk.