Subpulmonary Obstruction Due to Aneurismal Ventricular Septum in a Patient with Congenitally Corrected Transposition of the Great Arteries and Dextrocardia

摘要

Congenitally Corrected Transposition of the Great Arteries is usually associated with multiple cardiac defects. Some defects are complex and others are simple, such as atrial or ventricular septal defects. Membranous ventricular septal defects tend to close spontaneously; such closures are usually due to plastering down of one of the leaflets of the tricuspid valve, commonly referred to as formation of aneurysm of the membranous ventricular septum. Rarely, the aneurismal tissue occluding the ventricular septal defect may prolapse into the outflow tract of the morphologic left ventricle and cause significant obstruction to the pulmonary outflow tract, requiring surgical therapy. We report a case of severe subpulmonary stenosis due to an aneurysm of the membranous ventricular septum in a patient with Congenitally Corrected Transposition of Great Arteries and Dextrocardia.