Black hip: a rare case treated by total hip replacement

摘要

BACKGROUND AND OBJECTIVE: Ochronic arthropathy of hip (Black Hip) is a rare clinical manifestation of?congenital disorder of amino acid metabolism characterized by a classic triad: (1) degenerative arthritis, (2)?ochronotic pigmentation, and (3) urine that turns black on long standing or alkalinization. We report a case of?ochronic arthropathy of the left hip joint that was successfully treated by total hip arthroplasty. DESIGN AND SETTINGS: This is a case study conducted at PES Medical College, Andhra Pradesh, India. PATIENTS AND METHODS: A 60-year-old female patient came with a history of progressive pain in her left hip?joint for the last 8 months. She was diagnosed to be suffering from ochronic arthritis of left hip. RESULTS: After tissue confirmation she was operated with total hip replacement. At the end of 2 years, the patient was symptom free without any implant loosening. CONCLUSION: Ochronotic arthropathy is a rare metabolic disorder that can be underdiagnosed many a times.?Early management is only symptomatic, and advanced cases need surgical intervention. Vitamin preparations?are given because of the influence of vitamin C on tyrosine and phenylalanine metabolism. In the cases of severe?degenerative arthritis of hip, total hip replacement may be considered as a surgical option.