Biliary Atresia Associated with Polysplenia Syndrome, Situs Inversus Abdominus, and Reverse Rotation of Intestine

摘要

In 25% of cases of biliary atresia associated malformations are present; polysplenia constitute 10-50% of these associated anomalies. Biliary atresia found associated with polysplenia syndrome, heterotaxy, and reverse rotation of intestine, in isolation or in various combinations; however its association with polysplenia syndrome, situs inversus abdominus, and reverse rotation of gut in the same patient is not reported in English language literature [1,2].