Congenital Kyphosis in Thoracic Spine Secondary to Absence of Two Thoracic Vertebral Bodies

摘要

Congenital thoracic kyphosis at D6-D7 vertebral body level has been encountered in an 18-month-old boy without neurological deficit. The constellation of the spine malformation complex such as incomplete development of the vertebral bodies associated with defective ossification of the thoracic pedicles causing effectively the development of spinal cord injury at the kyphotic level of D6-D7 were present. Congenital kyphosis in thoracic spine secondary to absence of two thoracic vertebral bodies has been reported in a few studies. It is the absence and asymmetry of growth plates that may contribute to a congenital defect. Congenital Kyphosis refers to the normal convex curvature of the spine as it occurs in the thoracic and sacral regions since birth. Congenital kyphosis is an uncommon, but potentially devastating anomaly of the spine. It is one of the important aetiology for spinal cord compression leading to further neurological complications. Congenital kyphosis although rare, is more associated with neurological complication. Early identification not only helps in understanding its natural history but also helps in deciding its management.