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Chronic Periaortitis (Retroperitoneal Fibrosis) Concurrent with Recurrent Cutaneous Eosinophilic Vasculitis

机译:慢性反复性胸膜炎(腹膜纤维化)并发复发性皮肤嗜酸性粒细胞性血管炎

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摘要

Chronic periaortitis (CP) is usually accompanied by at least mild manifestations of systemic autoimmunity; however, skin manifestations are rare. Here, we report an 82-year-old woman presenting with a pruritic annular eosinophilic dermatosis that led to the diagnosis of recurrent cutaneous eosinophilic vasculitis (RCEV) coexisting with a latent CP. The present paper is reminder that a CP should be included as a potential differential diagnosis in the elaboration of patients with cutaneous vasculitis that is suspicious of underlying autoimmunity.
机译:慢性腹膜炎(CP)通常至少伴有轻度的全身自身免疫性表现。但是,皮肤表现很少见。在此,我们报道了一名82岁女性,患有瘙痒性环形嗜酸性粒细胞性皮肤病,导致诊断为潜在性CP并发的复发性皮肤嗜酸性粒细胞性血管炎(RCEV)。本文提醒您,在怀疑潜在的自身免疫性皮肤血管炎患者时,CP应作为潜在的鉴别诊断。

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