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Behcets Disease with Intracardiac Thrombus Presenting with Fever of Unknown Etiology

机译:心内血栓形成的白塞氏病病因不明

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摘要

A young male was referred to us for evaluation of fever of unknown origin (FUO). He had history of recurrent painful oral ulcers for one year and moderate to high grade fever, pustulopapular rash, and recurrent genital ulcers for 6 months and hemoptysis for 3 days. He was detected to have intracardiac thrombi and pulmonary arterial thrombosis along with underlying Behcet's disease (BD). Patient responded to high dose prednisolone (1 mg/Kg/day) along with monthly parenteral cyclophosphamide therapy. This case highlights the fact that BD is an important cause for pulmonary artery vasculitis with intracardiac thrombus formation, and such patients can present with FUO.
机译:一名年轻男性被转介给我们,以评估不明原因的发烧(FUO)。他有复发性口腔溃疡病史一年,中度至高烧,脓疱疹和复发性生殖器溃疡病史为6个月,咯血病史为3天。他被发现患有心内血栓和肺动脉血栓形成以及潜在的贝塞特氏病(BD)。患者对高剂量泼尼松龙(1毫克/千克/天)和每月肠胃外环磷酰胺治疗有反应。该病例凸显了以下事实:BD是导致心内血栓形成的肺动脉血管炎的重要原因,此类患者可出现FUO。

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