Institut des Maladies de l’Appareil Digestif;
Department of Gastroenterology and Digestive Oncology;
Nantes University Hospital;
Nantes Cedex 44093;
France;
Department of Gastroenterology;
Clinique Jules Verne;
Nantes 44300;
France;
Hermansky-Pudlak; syndrome; Acute; severe; colitis; Infliximab; Azathioprine; Inflammatory; bowel; disease; Case; report;