儿童原发性中枢神经系统血管炎的MRI表现

摘要

目的 通过磁共振成像(MRI)及磁共振血管成像(MRA)影像学表现探讨磁共振对儿童原发性中枢神经系统血管炎的诊断价值.方法 收集17例临床确诊儿童原发性中枢神经系统血管炎患儿的MRI、MRA影像资料,观察其影像表现并归纳分析影像特点.结果 17例患者中发病年龄2～13岁,临床表现为头晕头痛和不同程度的局灶性神经体征.MRI平扫显示病灶位于幕上16例,幕上下均累及l例;单侧8例,双侧9例.14例MRA显示,9例表现为血管节段性狭窄或闭塞,累及颅内多支血管,尤其集中于Willis环周边血管,5例MRA无异常改变.结论 结合临床特点,采用MRI和MRA检查可为临床诊断儿童中枢神经系统血管炎提供有价值的诊断依据.%Objective To retrospectively analyze MRI(Magnetic Resonance Imaging)and MRA(Magnetic Resonance Angiography)imaging features in children with primary angiitis of the central nervous system and to discuss MR diagnostic value of childhood primary angiitis of the central nervous system (cPACNS).Methods The characteristics of the imaging by collecting 17 the patient's MRI and MRA Imaging data with definite diagnosis of cPACNS were analyzed.Results The attack age among the 17 cases was from 2 to 13 years.The main clinical manifestations were dizziness,headache and different levels of focal neurological signs.16 cases were above the tentorium cerebelli,1 case was involving the tentorium cerebelli above and under.8 cases were on the single side of the brain.9 cases were on both sides of the brain.9 cases were characterized by vascular local stenosis or vascular occlusion,usually involving many intracranial vascular,especially concentrate on the surrounding of Willis ring.5 cases were no abnormal changes in MRA.Conclusion Combining with the clinical characteristics,we can provide valuable diagnostic basis of childhood primary angiitis of the central nervous system by using MRI and MRA.