原发性支气管肺淀粉样变性的CT诊断

摘要

目的:探讨支气管肺部淀粉样变性的影像学诊断及鉴别诊断.方法:收集5例经病理证实的支气管肺部淀粉样变性患者,分析其CT表现.结果:气管支气管型3例.CT表现为管壁不均质增厚,可见斑块状钙化灶,管腔内壁不光滑性狭窄；肺实质型2例,CT表现为主支气管旁单发团块,段支气管狭窄,周围肺组织萎缩,叶间裂增厚.结论:肺实质型CT表现单发或多发团块状软组织密度灶,气管支气管型CT表现为管壁增厚,可见颗粒或不规则钙化或“骨化岛”,具有一定特征.CT对肺部淀粉样变性的诊断具有重要价值.%Objective: To investigate the imaging diagnosis and differential diagnosis of bronchopulmonary amyloidosis. Methods:The CT manifestations of 5 patients with bronchopulmonary amyloidosis proved by pathology were retrospectively analysed. Results:The CT manifestations of tracheobronchial type in 3 cases were thickening of tracheobronchial wall, spot like calcification, stenosis of inner wall of pipeline. Those of pulmonary parenchyma type in 2 cases were the single mass in main bronchus aside, stenosis of segment bronchus, atrophy of pulmonary tissue around, thickening of fissure pleura. Conclusion:The CT manifestations of pulmonary parenchyma type were the single or multiple mass like soft tissue. The CT manifestations of tracheobronchial type were thickening of tracheobronchial wall, granule or irregular calcification, or ossific island, which have some features. CT has an important value in the diagnosis of bronchopulmonary amyloidosis.