布加综合征与妊娠

摘要

Budd-Chiari syndrome (BCS)is a rare liver disease,and there are mutual influences between BCS and pregnancy.The rela-tionship between BCS and pregnancy is systematically discussed,and the points we should pay attention to in the diagnosis and treatment of this disease are pointed out as follows:First,pregnancy is a risk factor for BCS;pregnant women with the clinical manifestations of portal hy-pertension and (or)inferior vena cava hypertension should be highly suspected of having BCS.Second,pregnancy is risky in BCS patients;pregnancy is allowable in BCS patients who have a stable condition after treatment,but they should be kept under rigorous surveillance dur-ing pregnancy and after delivery to avoid thrombosis recurrence.Third,BCS may lead to infertility in women;patients with unexplained in-fertility should be evaluated by abdominal ultrasound and computed tomography to clarify the diagnosis of BCS.%布加综合征是一种少见的肝脏疾病，其与妊娠之间相互影响。系统论述了布加综合征与妊娠的关系，并指出了在疾病诊断和治疗中的注意事项。其一，妊娠是布加综合征的危险因素。对于妊娠期间出现门静脉高压和（或）下腔静脉高压表现的患者，应高度怀疑合并布加综合征。其二，布加综合征患者妊娠具有一定的风险。经治疗病情稳定的患者可以妊娠，但孕期和产后须严密监查，以防止血栓复发。其三，布加综合征可导致女性不孕。原因不明的不孕患者应行腹部超声及CT检查，以排除布加综合征的可能。