the use of deferiprone, and methods for prophylaxis and / or friedreich's disease therapeutic result of a dysfunction of the intracellular iron processing

摘要

the present invention relates to a therapeutically active amount of deferiprone or deferasirox or salts of these compounds for physiological quality stabilization, the prevention, treatment or cure of a disease friedreich's iron induced in patients. the disease caused by damage to mitochondria induced by iron.the purpose of this amount and is preferentially active therapeutically to reduce the iron stores of the mitochondria. the present invention also relates to the treatment of other conditions affecting the brain as one of the key elements of the onset of the disease, is a dysfunction of the intracellular processing of iron.