Computerized cranial tomography was performed in 14 patients affected with hepatolenticular degeneration (4 presymptomatic and 10 with a hepatic form). 1 case showed brain stem atrophy with atypically located hypodense areas and another subject showed frontal atrophy with prevalence to the right side. The abnormalities found in another 7 cases were slight. In 5 patients, CT was normal.
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