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Annular bullous diseases

机译:环状大疱性疾病

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? 2022 Elsevier LtdAnnular bullous dermatoses represent an etiologically diverse group of cutaneous phenomena that present with a figurate morphology in association with vesicles and bullae. This group of diverse conditions consists of bullous pemphigoid; pemphigoid gestationis; epidermolysis bullosa simplex, Dowling-Meara type; linear immunoglobulin A bullous dermatosis; chronic bullous disease of childhood; anti-p200 pemphigoid; subcorneal pustular dermatosis; and immunoglobulin A pemphigus. Astute examination of clinical, histopathologic, and serologic features is crucial in distinguishing these bullous dermatoses. We review the clinical presentation, pathophysiology, histopathology, and treatments for each bullous annular disease to aid physicians in their recognition, diagnosis, and management.
机译:?2022 Elsevier Ltd环状大疱性皮肤病是一组病因学上多样化的皮肤现象,其形态表现为与水疱和大疱相关的形态。这组不同的疾病包括大疱性类天疱疮;类天疱疮妊娠;单纯性大疱性表皮松解症,Dowling-Meara型;线性免疫球蛋白 A 大疱性皮肤病;儿童慢性大疱性疾病;抗P200类天疱疮;角膜下脓疱性皮肤病;和免疫球蛋白A天疱疮。敏锐地检查临床、组织病理学和血清学特征对于鉴别这些大疱性皮肤病至关重要。我们回顾每种大疱性环状疾病的临床表现、病理生理学、组织病理学和治疗方法,以帮助医生识别、诊断和治疗。

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