Imaging of Gorlin-Goltz syndrome: Series of 2 cases

摘要

Gorlin–Goltz syndrome (GGS) is a rare autosomal dominant disorder with multisystemic involvement. Itis characterized by the triad of multiple baso‑cellular epitheliomas, odontogenic keratocysts (OKC) in thejaws and skeletal anomalies. Later, it was found that calcification of falx is also highly specific. We presentradiological findings in case series of two cases, one with multiple OKC, calcified falx, skin lesions, and fibrousdysplasia of sphenoid and second with multiple OKC, calcified falx, vertebral anomaly and medulloblastoma.