Desmoid-type fibromatosis arising in the inguinal region in a young woman: a case report from a histopathological perspective

摘要

Fibromatoses generally comprise a broad spectrum of myofibroblastic proliferation of similar histomorphology. Desmoid-type fibromatoses (desmoid tumors) are locally aggressive lesions which principally involve deep soft tissue structures. The author describes a 35-year-old female, who was found to have a nodular subcutaneous resistance arising in the upper portion of the right inguinal region. The tumor measured 40 x 25 x 15 mm and adhered to the aponeurosis of the abdominal internal oblique muscle. Histology revealed a dense mass of proliferating spindle-shaped myofibroblasts of uniform appearance. At the periphery, the lesion was poorly circumscribed and infiltrated an adjacent striated muscle. A diagnosis of desmoid-type fibromatosis was made. Desmoid tumor is a quite rare oncologic entity. Although it never metastasizes, it can lead to significant morbidity due to locally aggressive behaviour with a striking tendency to recur. Every patient once treated for deep fibromatosis requires long-term follow-up.