Objective: Rare diseaseBackground: Angiomyolipoma is a benign tumor composed of blood vessels, smooth muscle cells, and adipose tissue and has been described as belonging to the group of tumors of perivascular epithelioid cell origin (PEComa), com- monly found in the kidneys and strongly associated with tuberous sclerosis. Only a few cases of extra-renal an-giomyolipoma have previously been reported in the literature, most commonly in the liver. Adrenal angiomyo-lipoma is very rare, is usually asymptomatic, and is often found incidentally, with only 14 previously reported cases identified in the literature. Case Reports: We report two cases of adrenal angiomyolipoma that were identified by abdominal computed tomography (CT). The first case presented in a 36-year-old man and was an oval-shaped adrenal mass, measuring 5.2×4.2×3.1 cm. The second case presented in a 61-year-old woman and was a round-shaped mass measuring 8.6×9.5×8.1 cm. Both patients underwent adrenalectomy. Histopathology and immunohistochemistry confirmed the diagnosis of benign angiomyolipoma composed of adipose tissues, blood vessels, and smooth muscle cells.Conclusions: We present two rare cases of adrenal angiomyolipoma. We have reviewed the literature and identified 14 oth- er cases of adrenal angiomyolipoma, and discuss the clinical, radiological, and pathological features of this rare tumor.
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