Background Ebstein’s anomaly (EA) is mainly thought of as a right heart condition, however, congenital left-sided lesions canco-exist. Therefore, it is paramount to include the left side of the heart as part of a routine investigation in thesepatients. We present a 57-year-old symptomatic patient with EA and progressive tricuspid regurgitation (TR) associatedwith acquired left ventricular outflow obstruction (LVOTO). ...................................................................................................................................................................................................Case summary A 57-year-old women, known to have severe EA presented with shortness of breath and chest pain on exertionsecondary to progression of the tricuspid valve regurgitation and right ventricle dilatation leading to a dynamiccompression of the left outflow tract requiring surgical intervention. ...................................................................................................................................................................................................Discussion Left ventricular obstruction secondary to severe TR and dilation of the right ventricle can present and remain silentat rest but becoming significant on exertion. Therefore, we recommend that all patients with EA and significant TRundergo exercise echocardiography at regular intervals to specifically look for acquired dynamic LVOTO.
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