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首页> 外文期刊>Our Dermatology Online >Linear IgA bullous disease presenting as a Hailey-Hailey disease associated with Hashimoto thyroiditis: a case report
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Linear IgA bullous disease presenting as a Hailey-Hailey disease associated with Hashimoto thyroiditis: a case report

机译:线性IgA大疱性疾病表现为与桥本甲状腺炎相关的Hailey-Hailey病:一例报告

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摘要

Linear IgA bullous disease (LABD) is a rare autoimmune subepidermal bullous disease characterized by linear deposits of IgA anti-basement membrane zone antibodies. The skin lesions are variable: papular, vesicular, bullous, erythematous, edematous, and erythema multiforme-like, mimicking bullous pemphigoid, dermatitis herpetiformis, toxic epidermal necrolysis, mucous membrane pemphigoid or in described case - Hailey-Hailey disease. We present a case of a 17-year-old female patient diagnosed with LABD associated with Hashimoto thyroiditis.
机译:线性IgA大疱性疾病(LABD)是一种罕见的自身免疫性表皮下大疱性疾病,其特征在于线性沉积的IgA抗基底膜区抗体。皮肤病变是可变的:丘疹,水泡,大疱,红斑,水肿和多形红斑样,模仿大疱性天疱疮,疱疹样皮炎,中毒性表皮坏死,粘膜天疱疮或在描述的情况下-Hailey-Hailey病。我们介绍了一例17岁的女性患者,该患者被诊断出与桥本甲状腺炎相关的LABD。

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