Imperforate Anus (IA) is an abnormality of the anus and rectum that is present at birth. The infant is born without a normal rectal opening. Anorectal malformations occur in one in 5,000 live births. Anorectal and urogenital malformations are rarely fatal, although some associated anomalies (cardiac, renal) can be life threatening. The aim of this study is to determine congenital heart disease in babies with Imperforate Anus. Prospective study was carried out between February 1999 and January 2006 and it consisted of 93 consecutive children with IA. The study included children presenting with IA at the birth time. Echocardiography was done in all patients. Associated anomalies were studied and congenital heart anomalies were evaluated by Echocardiography. The study was undertaken in 93 patients with IA, 48(51.6%) boys and 44 girls. About 47(50.5%) of them had congenital heart anomalies. Echocardiography was performed in 87(93.5) of patients and were abnormal in 48.3% of studied cases. Mortality rate of studied patients with IA was 12.9%. Mean age of male patients was 1.02?0.146 day and Mean age of female patients was 1.02?1.51 day (p = 0.936). Mean age of died patients was 1.17?0.389 day and Mean age of improved patients was 1.02?1.51 day (p = 0.100). Atrial Septal Defect (ASD) was the most common associated cardiac anomaly. Associated anomalies such as congenital heart disease are present in a high percentage of patients with Anorectal malformations. Many of these associated anomalies are serious and long term prognosis of child with anorectal malformations more often depend on extent of these associated anomalies than on anorectal malformations itself. Systemic and radiological examination in neonatal period to detect associated anomalies at the earliest phase and should be managed immediately to prevent future morbidity and mortality.
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