A205 CONGENITAL ABSENCE OF THE PORTAL VEIN: DOES IT REALLY EXIST?

摘要

BackgroundCongenital portosystemic shunts are rare vascular malformation that can lead to pulmonary hypertension, encephalopathy and liver tumors. They were classified as type I(end-to-side portocaval fistula with no visible portal flow in the liver) and type II(side-to-side portocaval fistula)shunts.Type I shunts are often referred to a congenital absence of the portal vein(CAPV), and are still considered an indication for liver transplantation, whereas surgical or percutaneous closure is usually feasible for type II shunts.