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Cutis marmorata telangiectatica congenita with skin ulceration: a rare benign skin vascular malformation

机译:Cutis Marmorata Telangiectatica同性恋溃疡:罕见的良性皮肤血管畸形

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摘要

Cutis marmorata telangiectatica congenita (CMTC) is a sporadic congenital disorder characterised by localised or generalised cutaneous vascular anomaly. CMTC was first described in 1922 by Van Lohuizen as a pattern of reticulate erythema and telangiectasia infrequently associated with skin atrophy and/or ulceration.1 It is a rare benign skin lesion that is often apparent at birth with more than 50% of patients with CMTC having variations of associated defects. Body asymmetry is the most common (33%) associated anomaly reported.1
机译:Cutis Marmorata Telangiectatica Congenita(CMTC)是一种散发性先天性障碍,其特征是局部或广义皮肤血管异常。 CMTC首先于1922年由Van Lohuizen描述,作为网状红斑和卵巢疾病的模式,与皮肤萎缩和/或溃疡有关.1是一种罕见的良性皮肤病,在出生时常见于50%以上的CMTC患者。具有相关缺陷的变化。身体不对称是最常见的(33%)相关的异常报告

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