Orbital Rosai-Dorfman disease initially diagnosed as IgG4-related disease: a case report

摘要

MRI brain and orbits after multiple biopsies and worsening of ophthalmic symptoms. a T1-weighted post-contrast axial sequence at the level of the optic nerve demonstrating avid enhancement of the left orbital lesion with infiltration of the left lateral rectus muscle and obvious proptosis without associated optic nerve enhancement. b T2-weighted axial sequence showing the lobulated left orbital mass to be hypointense and without significant surrounding edema. c Diffusion-weighted imaging showing significant lesional diffusion restriction. d Coronal and (e) additional axial T1-weighted post-contrast images showing extension of the homogeneously-enhancing mass into the left maxillary sinus, pterygopalatine fossa, infratemporal fossa, and surrounding soft tissues