Double Aortic Arch with Atresia versus Interruption of Proximal Left Arch: Prospective Echocardiographic Diagnosis of an Extremely Rare Malformation

摘要

class="kwd-title">Keywords: Vascular rings, Double arch, Right arch class="head no_bottom_margin" id="sec1title">IntroductionVascular rings are rare malformations of pharyngeal arches that result in the trachea and esophagus being encompassed by the aortic arch and accompanying structures, potentially causing stridor and dysphagia. The most common variation is a double aortic arch; when both arches are patent, diagnosis is easily achieved by echocardiographic evaluation. When any portion of the double arch is absent, recognition is more difficult owing to absence of flow across that segment. We report a double arch with proximal left arch atresia versus interruption, which to the best of our knowledge is the first case to be diagnosed prospectively by echocardiogram.