Tessier 30 Facial Cleft Associated with Complete Duplication of Tongue: A Rare Entity

摘要

Background: Median cleft of mandible and lower lip is a rare anomaly [1]. Only a few cases have been reported in literature with different variations till now. Herein we report a patient with Tessier 30 cleft associated with complete duplication of tongue. Aim: We herein report this rare variant as it posed special challenges for its management by virtue of its uniqueness, late presentation and limited affordability of patient for standard treatment. Case Report: A 12 years old female reported to us with a chief complaint of a midline gap in the lower lip and mandible since birth. On examination under anaesthesia, we found that tongue was not bifid. There was complete duplication of the tongue. The case was planned for staged repair of the defect. In the same sitting, a repair of the soft tissues in the midline was performed. Conclusion: There are no specific guidelines in literature for management of such cases. This makes all these cases worth for reporting in order to guide treating surgeons.