Objective To improve the understanding of Meniere's disease in children and to achieve early diagnosis and treatment of Ménière's disease in children. Methods The clinical data of a child diagnosed as Ménière's disease depended on medical history, hearing results and inner ear MRI with Gadolinium enhancement were studied. Literatures about Ménière's disease in children were also reviewed. Results An 11 year old boy presented to our clinic due to episode of vertigo and tinni-tus of the left ear for 6 years. Vertigo The vertigo occurred 4-5 times a year and the hearing of the left ear was decreased gradu-ally. The child was treated in other hospital for many times and got no efficacy result. Ménière's disease was confirmed depen-ded on detailed medical history, hearing results and inner ear MRI with Gadolinium enhancement. The inner ear MRI exami-nation demonstrated an enlarged endolymphatic space in vestibule, which was consistent with the pathology of endolymphatic hydrops of Ménière's disease. Endolymphatic sac decompression was performed on this child. During more than 3 months' fol-low up, there was no recurrence of dizziness and hearing was preserved after surgery. Conclusion Endolymphatic hydrops ex-ists in the early stage in children with Ménière's disease. Children may give inadequate information of the clinical characters of dizziness, which may mislead to the difficult to diagnosis. Inner ear MRI examination with Gadolinium enhancement can detect endolymphatic hydrops, and provide objective evidence for the diagnosis of Ménière's disease.%目的 提高对儿童梅尼埃病的认识,以早期诊断、治疗.方法 回顾性分析1例经内耳钆剂MRI造影确诊的儿童梅尼埃病患者资料,并复习国内外相关文献.结果 患儿11岁,因发作性眩晕伴左耳耳鸣6年余就诊,眩晕每年发作约4~5次,左耳听力渐下降.多次就诊外院,行头颅MRI等检查未见异常,药物控制眩晕效果不佳.入我院后,结合病史、听力学检查结果,进一步行内耳钆剂MRI造影示双侧膜迷路积水,确诊梅尼埃病.行内淋巴囊减压术,术后随访3个月眩晕未再发作,听力未再继续减退.结论 因儿童梅尼埃病患者内耳积水处于病变初始阶段,尚未引起症状,且患儿对症状的描述欠准确,导致诊断困难.内耳钆剂MRI造影检测到内耳积水可为本病诊断提供相对客观的证据.
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