作者报告多器官旋转不良综合征2例,1例为生后36天女婴,经手术探查证实肝位左上腹,脾呈球形位中腹部,胃及十二指肠反向,伴环状胰腺及十二指肠前门静脉.行胃空肠吻合术后痊愈出院.另1例生后26天男婴,手术证实胃、十二指肠反位,伴环状胰腺及十二指肠前门静脉,胆囊呈分叉状.行胃空肠吻合治疗.作者还讨论了多器官旋转不良综合征的临床特点及治疗原则.%The viscers involved in multiple organ malrotation syndrome(MOMS)are the pancreas,liver,spleen,stomach and duodenum which are in abnormal location and/or obstruction.The abnormalities have been generally occured when the fetus develops at 5-6 weeks of gestation.The diagnosis of MOMS should be considered whenever the triad of iritestinal obstruction,left-side liver in the presence of laevocardia and reversed double bubble is encountered in a baby.The authers report 2 cases.The first case was a thirty-six.day old girl.Laparotomy confilmed the diagnosis of MOMS.The liver was on the left side.The spleen was located in the right hypochondrium.The duodenum and stomach were inverse with an annular pancreas and preduodenum portal vein.She was operated on by gastrojejunostomy and discharged after one month.The second one was a twentysix-day old boy.Laparotomy showed the same findings including an accessory pancreas on the pyloric antrum and a cleft gallbladder.A gastrojejunostomy was carried out.The postoperative recovery was uneventful.
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