目的:总结三房心临床特点、合并畸形及影像学诊断特点.方法:1993年1月至2005年6月共收治23例三房心患者,男13例,女10例,年龄0.3～38(9.6±10.0)岁.均为左型三房心,其中21例获得手术证实,完全型15例,部分型6例.心电图检查:电轴右偏18例,电轴偏左1例,电轴正常4例.胸片检查:18例肺血增多.结果:术前经超声检查确诊12例(52.2％),10例行心导管确诊4例(40％).21例中16例(76.2％)合并其它畸形,合并房间隔缺损14例(66.7％)、部分肺静脉异位引流6例(28.6％)、肺动脉瓣狭窄3例(14.3％),永存左上腔3例(14.3％).结论:三房心临床表现多样,合并畸形发生率较高,彩色超声心动图检查有较高诊断价值.心导管检查对合并畸形诊断率较高,对合并畸形者强调术中探查.%To summarize clinical feature, complicated abnormities and imaging diagnosis of cor triatriatum in 23 cases. Methods: From Jan 1993 to Jun 2005, a total of 23 patients with cor triatriatum [13 males and 10 females with age 0. 3~38 (9. 6 ± 10. 0) years] were enrolled in the study. All cases were cor triatriatum laevns. A total of 21 patients were identified by surgery. There were 15 cases with complete cor triatriatum and six cases with incomplete cor triatriatum. Electrocardiography measurement showed that there were 18 patients with right axis deviations, one patient with left axis deviation and four patients with normal electric axis. A total of 18 cases showed lung congestion in X-ray examination. Results: A total of 12 cases (52. 2%) were diagnosed by echocardiography before surgery. There were four cases (40%) diagnosed by cardiac catheterization in 10 cases. A total of 16 cases (76. 2%) accompanied other abnormities: atrial septal defect (n= 14, 66. 7%), partial anomalous pulmonary venous drainage (n = 6, 28.6%), pulmonary valve stenosis (n = 3, 14.3%), persistent left superior vena cava (n = 3, 14. 3%). Conclusion: Cor triatriatum has various manifestations in clinical feature and incidence rates of complicated malformations are high. Color-coded Doppler echocardiography possesses high value in diagnosis of cor triatriatum, but it's hard to diagnose cases with complicated malformations. Cardiac catheterization possesses high diagnosis rate in those with abnormities. Surgical exploration is very important in patients with cor triatriatum complicated malformations.
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