The management of Scimitar syndrome in adulthood is controversial, with no guidelines for surgical correction. We present the case of a 66-year-old woman who presented late in life with Scimitar syndrome and a significant left-to-right shunt. We describe repair using an intra-atrial conduit from the anomalous vein to the foramen ovale, with a successful outcome.Scimitar syndrome was first described by Cooper in 1836. This syndrome of partial or total anomalous pulmonary venous return of the right pulmonary veins to the inferior vena cava (IVC) was named 'Scimitar syndrome' by Neill in 1960 because the abnormal vessel can often be seen as a curvilinear density along the right heart border on plain chest radiography. Additional features in this syndrome such as hypoplasia and abnormalities of the vascular supply to the right lung, dextrocardia and abnormalities of bronchial segmentation are common; bronchiectasis is rare [1].
展开▼
