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首页> 外文期刊>JAMA dermatology >Cholesterol embolization syndrome with an atypical proximal presentation simulating calciphylaxis
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Cholesterol embolization syndrome with an atypical proximal presentation simulating calciphylaxis

机译:胆固醇栓塞综合症,近端表现不典型,模拟钙化

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摘要

Cholesterol embolization syndrome (CES) is associated with endovascular procedures or anticoagulation, which disrupt ath-eromatous plaques within large arteries releasing cholesterol crystals. These crystals lodge in the vasculature of various organs, most commonly the skin. Cutaneous involvement classically presents in the distal lower extremities as livedo reticu-laris (49%), gangrene (35%), cyanosis (28%), ulceration (17%), nodules (10%), purpura (9%), and splinter hemorrhages. We report a case of CES with proximal cutaneous lesions mimicking calciphylaxis.
机译:胆固醇栓塞综合症(CES)与血管内手术或抗凝有关,后者破坏大动脉内的哮喘气菌斑并释放出胆固醇晶体。这些晶体存在于各种器官的血管中,最常见的是皮肤。皮肤受累通常在下肢远端表现为网状网纹(49%),坏疽(35%),紫osis(28%),溃疡(17%),结节(10%),紫癜(9%)和碎片出血。我们报告一例CES的近端皮肤病变模仿拟茶碱。

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