色素失禁症1例

摘要

色素失禁症是一种罕见的主要发生于女婴的 X 连锁遗传性皮肤病。本文报道1例出生时躯干及四肢即出现红斑和脓疱性皮损，组织病理符合色素失禁症。%Incontinentia pigmenti is a rare X-linked genodermatosis which affects mainly female neonates. A female infant with erythema and pustules lesions on trunk and limbs was presented. Biopsy revealed the diagnosis of incontinentia pigmenti.