Pleuropulmonary blastoma(PPB) is a very rare and very aggressive malignant tumor that affects childrenand adults. Though its presentation in children has been reported in literature,incidence is very low as compared to adults. This neoplasm is characterized on histology by primitiveblastema and a malignant mesenchymal stroma that often demonstrates multidirectionaldifferentiation. Even though availability of multimodal therapy, the prognosis of patients with PPB remains poor.
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